Thursday, October 20, 2011

Sweet’s Syndrome with Postinflammatory Elastolysis and Takayasu Arteritis in a Child: A Case Report and Literature Review


Abstract:  Sweet’s syndrome (SS) is an uncommon condition characterized by recurrent painful cutaneous inflammatory eruptions. It is rare in childhood and has a broad range of extracutaneous manifestations. We describe a child presenting with SS and postinflammatory elastolysis who subsequently developed aortitis complicated by aortic dilatation requiring surgical intervention. Histologic features of the aorta were consistent with Takayasu arteritis (TA). Our case and previously reported cases of pediatric SS complicated by aortitis all demonstrate striking clinical similarities in that all have been associated with postinflammatory elastolysis of involved skin and ...

Sweet’s Syndrome with Postinflammatory Elastolysis and Takayasu Arteritis in a Child: A Case Report and Literature Review is a post from: Skincare




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