Sunday, March 27, 2011

A Case of Congenital Pigmented Dermatofibrosarcoma Protuberans (Bednar Tumor) in a Patient with Fanconi Anemia


Abstract:  Bednar tumor is a rare pigmented variation of dermatofibrosarcoma protuberans, present in 1 to 5% of all patients with dermatofibrosarcoma protuberans. No significant clinicopathologic differences exist between Bednar tumor and conventional dermatofibrosarcoma protuberans apart from the presence of scattered nonneoplastic pigmented dendritic cells in the former. Although most dermatofibrosarcoma protuberans occur in adults, they may be rarely present at birth. Fanconi anemia is a genetically heterogeneous chromosomal instability syndrome, characterized by multiple congenital anomalies, progressive bone marrow failure, and a predisposition to malignancy. We describe here a patient with ...

A Case of Congenital Pigmented Dermatofibrosarcoma Protuberans (Bednar Tumor) in a Patient with Fanconi Anemia is a post from: Skincare




A Case of Congenital Pigmented Dermatofibrosarcoma Protuberans (Bednar Tumor) in a Patient with Fanconi Anemia via BuzzBlazer.com

No comments:

Post a Comment